Fruits

    Fruits that are  medium high in methionine  25-50 mg of methionine/ 100 gm of the product)  Navel orange, Mandarin Oranges, Fruits that are Low  in methionine (less than 25mg of methionine/ 100 gm of the product) Watermelon, cantaloupe, Honeydew melon, apples, pears, Cranberries, Raspberries, Blueberries, Strawberries, mango, plums, Dates (dried), peaches,

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Vegetables

  Vegetables that are High  in methionine/ per 100 gm (more than 25mg – 50mg of methionine/ 100 gm of the product) Broccoli, Mushroom, Cauliflower, Avocado, Bean sprouts, potatoes, Vegetables that are High  in methionine/ per 100 gm (more than 50mg of methionine/ 100 gm of the product) Spinach, Green Peas, corn

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MSUD (Maple Syrup Urine Disease)

MSUD is an autosomal recessive metabolic disorder affecting branched-chain amino acids. It is one type of organic academia. The condition gets its name from the distinctive sweet odor of affected infants’ urine, particularly prior to diagnosis, and during times of acute illness. Maple syrup urine disease can be classified by

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Food and Formula Vendors

Vendor  Products Website 1 ABBOTT LAB Formula https://abbottnutrition.com/therapeutic 2 CAMBROOKE THERAPEUTICS Formula & Food Products https://www.cambrooke.com/ 3 FLAVIS Food Products https://www.flavis.com/en 4 LILSDIETARY Food Products https://lilsdietary.com/ 5 MEDJOHNSON NUTRITION Formula https://www.meadjohnson.com/ 6 NUTRICIA METABOLICS Formula & Food Products http://medicalfood.com/ 7 PKU PERSPECTIVES Food Products https://www.pkuperspectives.com/ 8 PHARMA NORTH AMERICA Formula

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General Approach

Low-protein food products are recommended to persons with particular types of metabolic disorders such as  Homocystinuria (HCU), Phenylketonuria (PKU), Methylmalonic Acidemia(MMA) and Tyrosinemia. Each of these disorders require food products which are low in particular type of amino-acid. i.e. methonine in the case of HCU, phenylalanine in the case of

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Tyrosinemia

Tyrosinemia is an error of metabolism, usually inborn, in which the body cannot effectively break down the amino acid tyrosine. Symptoms of untreated tyrosinemia include liver and kidney disturbances. Without treatment, tyrosinemia leads to liver failure. Today, tyrosinemia is increasingly detected on newborn screening tests before any symptoms appear. With

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